Multimodality Imaging of Constrictive Pericarditis in H Syndrome

Multimodality Imaging of Constrictive Pericarditis in H Syndrome Publisher Pubmed

Malakan Rad E¹ ; Yaghmaei B² ; Ziaee V^{3, 4, 5} ; Beirami F² ; Pouraliakbar H⁶

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1. Department of Pediatric Cardiology, Childrenâ€™s Medical Center (Pediatric Center of Excellence), Tehran University of Medical Sciences, Tehran, Iran
2. Department of Pediatric Intensive Care, Childrenâ€™s Medical Center (Pediatric Center of Excellence), Tehran University of Medical Sciences, Tehran, Iran
3. Department of Pediatrics, Tehran University of Medical Science, Tehran, Iran
4. Childrenâ€™s Medical Center, Pediatric Center of Excellence, Tehran, Iran
5. Pediatric Rheumatology Research Group, Rheumatology Research Center, Tehran University of Medical Science, Tehran, Iran
6. Rajaie Cardiovascular Medical and Research Center, Niayesh Highway, Tehran, Iran

Source: Echocardiography Published:2021

Abstract

This is the first report of constrictive pericarditis (CP) in a 16-year-old boy with H syndrome with pericardial involvement predominantly over the right ventricle with favorable response to anti-inflammatory treatment. H syndrome, first reported in 2008, is a new auto-inflammatory syndrome with multiorgan involvement due to mutation in the SLC29A3 gene. We described the echocardiographic characteristics of asymmetric pericardial involvement and presented the cardiac computed tomography angiographic and magnetic resonance imaging findings. We reviewed the echocardiographic signs of CP, introduced tricuspid E/A respiratory alternans as a novel echocardiographic sign of right ventricular dominant CP, and explained the underlying mechanism. © 2021 Wiley Periodicals LLC

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Style	Citing Format
MLA	Malakan Rad E, et al.. "Multimodality Imaging of Constrictive Pericarditis in H Syndrome." Echocardiography, vol. 38, no. 6, 2021, pp. 1021-1032.
APA	Malakan Rad E, Yaghmaei B, Ziaee V, Beirami F, Pouraliakbar H (2021). Multimodality Imaging of Constrictive Pericarditis in H Syndrome. Echocardiography, 38(6), 1021-1032.
Chicago	Malakan Rad E, Yaghmaei B, Ziaee V, Beirami F, Pouraliakbar H. "Multimodality Imaging of Constrictive Pericarditis in H Syndrome." Echocardiography 38, no. 6 (2021): 1021-1032.
Harvard	Malakan Rad E et al. (2021) 'Multimodality Imaging of Constrictive Pericarditis in H Syndrome', Echocardiography, 38(6), pp. 1021-1032.
Vancouver	Malakan Rad E, Yaghmaei B, Ziaee V, Beirami F, Pouraliakbar H. Multimodality Imaging of Constrictive Pericarditis in H Syndrome. Echocardiography. 2021;38(6):1021-1032.
BibTex	@article{ author = {Malakan Rad E and Yaghmaei B and Ziaee V and Beirami F and Pouraliakbar H}, title = {Multimodality Imaging of Constrictive Pericarditis in H Syndrome}, journal = {Echocardiography}, volume = {38}, number = {6}, pages = {1021-1032}, year = {2021} }
RIS	TY - JOUR AU - Malakan Rad E AU - Yaghmaei B AU - Ziaee V AU - Beirami F AU - Pouraliakbar H TI - Multimodality Imaging of Constrictive Pericarditis in H Syndrome JO - Echocardiography VL - 38 IS - 6 SP - 1021 EP - 1032 PY - 2021 ER -

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