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Erdheim-Chester Disease With Long-Standing Diabetes Insipidus and Generalized Edema Publisher



Naji FS1 ; Hajmiri MS1 ; Mazari Z2 ; Salahshour F3 ; Soleimani V2 ; Nakhjavani M1 ; Hemmatabadi M1
Authors
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Authors Affiliations
  1. 1. Department of Endocrinology, Endocrinology and Metabolism Research Center (EMRC), Vali-Asr Hospital, Imam Khomeini Complex Hospital, Tehran University of Medical Sciences, Tehran, Iran
  2. 2. Cancer Institute, Department of Pathology, Imam Khomeini Complex Hospital, Tehran University of Medical Sciences, Tehran, Iran
  3. 3. Department of Radiology, Imam Khomeini Complex Hospital, Tehran University of Medical Sciences, Tehran, Iran

Source: Clinical Case Reports Published:2021


Abstract

Erdheim-Chester disease (ECD) is a rare non-Langerhans histiocytosis. ECD is detected more frequently due to increased awareness of healthcare providers and improved diagnostic tools. This report describes a 51-year-old woman with a history of weakness, bone pain, xanthelasma palpebrarum, and diabetes insipidus. ECD is a multisystemic condition with a poor prognosis. This disease should be considered in patients with diabetes insipidus, bone pain, and multiorgan involvements. © 2021 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd.