Tehran University of Medical Sciences

Science Communicator Platform

Stay connected! Follow us on X network (Twitter):
Share this content! On (X network) By
Mixed Inferior Sinus Venosus and Secundum Atrial Septal Defects With Mixed Partial Anomalous Pulmonary and Systemic Venous Drainage: Key Insights and Practical Implications Publisher



Malakan Rad E1 ; Radmehr H2 ; Taghizadeh A3 ; Pouraliakbar H4 ; Radmehr E5, 6, 7
Authors
Show Affiliations
Authors Affiliations
  1. 1. Department of Pediatrics, Fetal and Pediatric Cardiovascular Research Center, Children’s Medical Center, Imam Khomeini Hospital Complex, School of Medicine, Tehran University of Medical Sciences, Tehran, Iran
  2. 2. Department of General Surgery, Fetal and Pediatric Cardiovascular Research Center, Children’s Medical Center, Imam Khomeini Hospital Complex, School of Medicine, Tehran University of Medical Sciences, Tehran, Iran
  3. 3. Department of Anesthesiology, Children’s Medical Center, Imam Khomeini Hospital Complex, School of Medicine, Tehran University of Medical Sciences, Tehran, Iran
  4. 4. Rajaie Cardiovascular Medical and Research Institute, Tehran, Iran
  5. 5. Colorectal Research Center, Imam Khomeini Hospital Complex, Tehran University of Medical Sciences, Tehran, Iran
  6. 6. Universal Scientific Education and Research Network (USERN), Yerevan, Armenia
  7. 7. School of Medicine, Tehran University of Medical Sciences, Tehran, Iran

Source: Journal of Tehran University Heart Center Published:2024


Abstract

Mixed atrial septal defects (ASDs) involving inferior vena cava (IVC)-type sinus venosus and secundum types and mixed partial anomalous pulmonary, systemic, and hepatic venous drainage are rare. We describe a 3-year-old acyanotic boy who presented with a large mixed inferior sinus venosus and secundum-type ASD. He exhibited an abnormal connection between the right upper pulmonary vein and the right atrium. Additionally, the IVC and a hepatic vein drained abnormally into the left atrium. The patient also had valvular and supravalvular pulmonary stenosis, as well as a small patent ductus arteriosus. The ASD was surgically closed using a pericardial patch, positioned lower than usual to reroute the IVC and hepatic vein flow into the right atrium. The surgery was successful, with no residual lesions or complications. The patient recovered without issues and was discharged smoothly. At the 6-month follow-up, the child’s cardiac examination and oxygen saturation were normal. Furthermore, echocardiography confirmed normal drainage of the systemic and hepatic veins into the right atrium. © 2024 Tehran University of Medical Sciences. Published by Tehran University of Medical Sciences.