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Case Study: Temperature-Sensitive Recurrent, Reversible Auditory Neuropathy in Two Iranian Siblings Publisher



Yazdani N1 ; Ahadi M2
Authors
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Authors Affiliations
  1. 1. Department of Otorhinolaryngology, Otorhinolaryngology Research Center, Amir-Alam Hospital, Tehran University of Medical Sciences, Tehran, Iran
  2. 2. Department of Audiology, Rehabilitation Research Center, School of Rehabilitation Sciences, Iran University of Medical Sciences, Tehran, Iran

Source: Iranian Rehabilitation Journal Published:2021


Abstract

Two sibling cases with a temperature-sensitive form of auditory neuropathy from a consanguineous marriage of Iranian descent have been described. They complained about the temporary loss of hearing and compromised speech comprehension after a slight fever or elevating the body temperature by vigorous exercises. A series of tests including brain MRI, pure-tone audiometry, speech audiometry in quiet and noise, tympanometry, reflexometry, TEOAEs, cochlear microphonic, and ABR were performed in a 24-hours interval at both febrile and afebrile states, and results are reported here. This report is the first example of temperature-sensitive auditory neuropathy in this geographical region © 2021. Iranian Rehabilitation Journal. All Rights Reserved.