Paraneoplastic Pemphigus Associated With Inflammatory Myofibroblastic Tumour of the Mediastinum: A Favourable Response to Treatment and Review of the Literature

Paraneoplastic Pemphigus Associated With Inflammatory Myofibroblastic Tumour of the Mediastinum: A Favourable Response to Treatment and Review of the Literature Publisher Pubmed

Ghandi N^{1, 2} ; Ghanadan A^{3, 4} ; Azizian MR⁵ ; Hejazi P^{1, 2} ; Aghazadeh N^{1, 2} ; Tavousi P^{1, 2} ; Daneshpazhooh M^{1, 2}

Show Affiliations

1. Autoimmune Bullous Diseases Research Centre, Razi Hospital, Tehran University of Medical Sciences, Tehran, Iran
2. Department of Dermatology, Razi Hospital, Tehran University of Medical Sciences, Tehran, Iran
3. Dermatopathology Department, Razi Hospital, Tehran University of Medical Sciences, Tehran, Iran
4. Pathology Department, Cancer Institute, Imam Khomeini Complex Hospital, Tehran, Iran
5. Dermatopathology Department, Shahriar Hospital, Tehran, Iran

Source: Australasian Journal of Dermatology Published:2015

Abstract

Paraneoplastic pemphigus (PNP) is an autoimmune blistering disorder that occurs in association with an underlying neoplasm. Inflammatory myofibroblastic tumour (IMT) is a rare low-grade sarcoma of fibroblasts and myofibroblasts associated with inflammatory cells, most commonly occurring in the lung. In this study, a case of PNP associated with IMT of the mediastinum is reported. The patient had a favourable outcome following surgical resection and treatment with a systemic steroid, azathioprine, and i.v. immunoglobulin. The occurrence of PNP with sarcomas, specifically IMT, is noteworthy although it is not well studied in the existing literature. © 2014 The Australasian College of Dermatologists.

2. S2k Guidelines on the Management of Paraneoplastic Pemphigus/Paraneoplastic Autoimmune Multiorgan Syndrome Initiated by the European Academy of Dermatology and Venereology (Eadv), Journal of the European Academy of Dermatology and Venereology (2023)

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Maryam Daneshpajooh (1)

Arghavan Azizpoor (1)

Style	Citing Format
MLA	Ghandi N, et al.. "Paraneoplastic Pemphigus Associated With Inflammatory Myofibroblastic Tumour of the Mediastinum: A Favourable Response to Treatment and Review of the Literature." Australasian Journal of Dermatology, vol. 56, no. 2, 2015, pp. 120-123.
APA	Ghandi N, Ghanadan A, Azizian MR, Hejazi P, Aghazadeh N, Tavousi P, Daneshpazhooh M (2015). Paraneoplastic Pemphigus Associated With Inflammatory Myofibroblastic Tumour of the Mediastinum: A Favourable Response to Treatment and Review of the Literature. Australasian Journal of Dermatology, 56(2), 120-123.
Chicago	Ghandi N, Ghanadan A, Azizian MR, Hejazi P, Aghazadeh N, Tavousi P, Daneshpazhooh M. "Paraneoplastic Pemphigus Associated With Inflammatory Myofibroblastic Tumour of the Mediastinum: A Favourable Response to Treatment and Review of the Literature." Australasian Journal of Dermatology 56, no. 2 (2015): 120-123.
Harvard	Ghandi N et al. (2015) 'Paraneoplastic Pemphigus Associated With Inflammatory Myofibroblastic Tumour of the Mediastinum: A Favourable Response to Treatment and Review of the Literature', Australasian Journal of Dermatology, 56(2), pp. 120-123.
Vancouver	Ghandi N, Ghanadan A, Azizian MR, Hejazi P, Aghazadeh N, Tavousi P, et al.. Paraneoplastic Pemphigus Associated With Inflammatory Myofibroblastic Tumour of the Mediastinum: A Favourable Response to Treatment and Review of the Literature. Australasian Journal of Dermatology. 2015;56(2):120-123.
BibTex	@article{ author = {Ghandi N and Ghanadan A and Azizian MR and Hejazi P and Aghazadeh N and Tavousi P and Daneshpazhooh M}, title = {Paraneoplastic Pemphigus Associated With Inflammatory Myofibroblastic Tumour of the Mediastinum: A Favourable Response to Treatment and Review of the Literature}, journal = {Australasian Journal of Dermatology}, volume = {56}, number = {2}, pages = {120-123}, year = {2015} }
RIS	TY - JOUR AU - Ghandi N AU - Ghanadan A AU - Azizian MR AU - Hejazi P AU - Aghazadeh N AU - Tavousi P AU - Daneshpazhooh M TI - Paraneoplastic Pemphigus Associated With Inflammatory Myofibroblastic Tumour of the Mediastinum: A Favourable Response to Treatment and Review of the Literature JO - Australasian Journal of Dermatology VL - 56 IS - 2 SP - 120 EP - 123 PY - 2015 ER -

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