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Patient With Crouzon Syndrome Treated With Modified Le Fort Iii Osteotomy Without Previous Orthodontic Treatment: Case Report and a Review of the Literature Publisher



Mohammadi F1 ; Javanmard A2 ; Mojtahedi H1
Authors
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Authors Affiliations
  1. 1. Craniomaxillofacial Research Center, Oral and Maxillofacial Surgery Department, Shariati Hospital, Tehran University of Medical Sciences, Tehran, Iran
  2. 2. Department of Prosthodontics and Dental Research Center, Faculty of Dentistry, Tehran University of Medical Sciences, Tehran, Iran

Source: Case Reports in Dentistry Published:2020


Abstract

Crouzon syndrome is the most common type of craniofacial dysostosis anomaly which presents a great challenge for clinicians since birth. Multiple synostoses in the sutures of the cranial base in this syndrome result in the hypoplasia of the midface, shallow orbits, a short nasal dorsum, maxillary hypoplasia, and, in severe cases, obstruction of the upper airways. Apart from esthetic and functional problems, these patients suffer from various psychological problems which mandate correction of midface deformities at younger ages. The aim of this report is to describe the case of a 26-year-old female patient with Crouzon syndrome displaying severe midface hypoplasia and proptosis with no history of orthodontic treatment, who was treated with modified Le Fort III osteotomy with a coronal and intraoral approach without periocular incisions. © 2020 Farnoosh Mohammadi et al.