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Unexpectedly Large Myoepithelioma-Like Tumor of the Vulvar Region With Two Local Recurrences: A Rare Case Report and Review of the Literature Publisher



Aminimoghaddam S1 ; Sarmadi S2 ; Kashian M3 ; Sarchami N4
Authors
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Authors Affiliations
  1. 1. Department of Obstetrics and Gynecology, School of Medicine, Iran University of Medical Sciences, Tehran, Iran
  2. 2. Department of Pathology, Yas Women Hospital, Tehran University of Medical Sciences, Tehran, Iran
  3. 3. Iran University of Medical Sciences, Tehran, Iran
  4. 4. Department of Obstetrics and Gynecology, Firouzgar Hospital, Iran University of Medical Sciences, Tehran, Iran

Source: Gynecologic Oncology Reports Published:2023


Abstract

Myoepithelioma-like tumors of the vulvar region (MELTVR) are rare. Only a limited number of MELTVRs are reported in the literature, and various aspects of this lesion still need to be clarified. In this study, we reported a case of MELTVR in a 46-year-old female. The uniqueness of the present case was its large size (12 cm) compared to the MELTVRs reported in earlier studies, the presence of two separate but attached lesions (one in labia majora and one in the mons pubis), and two recurrences within ten years after wide local excision. The second recurrence was managed with wide excision, and the patient remained disease-free during the two-year follow-up. This case highlights the local aggressiveness of MELTVR and the necessity of resection with an adequate margin. It also urges more awareness regarding the differential diagnosis of MELTVR with other lesions of the vulva, particularly when located in the labia majora and mons pubis. © 2023