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Kartagener Syndrome With Focal Segmental Glomerulosclerosis Pubmed



Momeni A1 ; Doroushi B2 ; Taheri N3
Authors
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Authors Affiliations
  1. 1. Division of Nephrology, Department of Internal Medicine, Shahrekord University of Medical Sciences, Shahrekord, Iran
  2. 2. Division of Rheumatology, Department of Internal Medicine, Shahrekord University of Medical Sciences, Shahrekord, Iran
  3. 3. Department of Pathology, Isfahan University of Medical Sciences, Isfahan, Iran

Source: Iranian Journal of Kidney Diseases Published:2013


Abstract

Primary ciliary dyskinesia is characterized by congenital impairment of mucociliary clearance. Kartagener syndrome (KS) is a clinical variant of primary ciliary dyskinesia which is involved in situs inversus associated with chronic respiratory infections. In addition, glomerular disease in KS syndrome is rare and reported cases are limited. We had a 27-year-old female patient with KS who presented with proteinuria, hematuria, normal kidney function, and a family history of systemic lupus erythematosus. Kidney biopsy showed segmental scar with adhesion to Bowman capsule, which was indicative of focal segmental glomerulosclerosis.
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1. Trpc6 Mutational Analysis in Iranian Children With Focal Segmental Glomerulosclerosis, Iranian Journal of Kidney Diseases (2018)
2. Prediction of Kidney Survival in Children With Primary Focal Segmental Glomerulosclerosis (A Two-Center Study), Journal of Research in Medical Sciences (2007)
3. Vascular Lesions in Lupus Nephropathy, Journal of Isfahan Medical School (2014)
4. A Study on Variants of Focal Segmental Glomerulosclerosis and Their Relationship With Various Biochemical and Demographic Parameters in Kidney Biopsies; a Single Center Study, Journal of Nephropharmacology (2019)
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