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Adult Onset Still Disease Associated With Endogenous Lipoid Pneumonia Publisher Pubmed



Sami R1 ; Zohal M2 ; Mohammadi F3
Authors
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Authors Affiliations
  1. 1. Department of Internal Medicine, Isfahan University of Medical Sciences, Isfahan, Iran
  2. 2. Pulmonary Diseases Metabolic Diseases Research Center, Qazvin University of Medical Sciences, Velayat Hospital, 22 Bahman Blvd., Elahiyeh, Qazvin, Iran
  3. 3. Department of Pathology, National Research Institute of Tuberculosis and Lung Disease, Shahid Beheshti University of Medical Sciences, Tehran, Iran

Source: Advances in Respiratory Medicine Published:2019


Abstract

Cholesterol pneumonia or endogenous lipid pneumonia (ELP) is a rare disease that can occur in the context of a systemic disease or following a bronchial obstruction. It is characterized by a wide range of diverse symptoms and various disease course. The present report introduces a young woman diagnosed with adult onset still disease three years ago, who has been referred with macrophage activation syndrome (MAS). She underwent biopsy due to dyspnea and a crazy paving pattern in HRCT of the lungs, leading to the diagnosis of lipoid pneumonia based on the interstitial lymphocytic inflammation and cholesterol granulomas. So far, there has been no report indicating MAS associated with cholesterol pneumonia. This is the second case reporting ELP in the adult onset still disease. © 2019, Via Medica. All rights reserved.