International Bullous Diseases Group: Consensus on Diagnostic Criteria for Epidermolysis Bullosa Acquisita

International Bullous Diseases Group: Consensus on Diagnostic Criteria for Epidermolysis Bullosa Acquisita Publisher Pubmed

Prostsquarcioni C^{1, 2, 3} ; Caux F¹ ; Schmidt E⁴ ; Jonkman MF⁵ ; Vassileva S⁶ ; Kim SC⁷ ; Iranzo P⁸ ; Daneshpazhooh M⁹ ; Terra J⁵ ; Bauer J¹⁰ ; Fairley J¹¹ ; Hall R¹² ; Hertl M¹³ ; Lehman JS¹⁴ Show All Authors

Prostsquarcioni C^{1, 2, 3}
Caux F¹
Schmidt E⁴
Jonkman MF⁵
Vassileva S⁶
Kim SC⁷
Iranzo P⁸
Daneshpazhooh M⁹
Terra J⁵
Bauer J¹⁰
Fairley J¹¹
Hall R¹²
Hertl M¹³
Lehman JS¹⁴
Marinovic B¹⁵
Patsatsi A¹⁶
Zillikens D⁴
Werth V¹⁷
Woodley DT¹⁸
Murrell DF¹⁹

Show Affiliations

1. Department of Dermatology and Referral Center for Autoimmune Bullous Diseases, APHP, Avicenne Hospital, Bobigny, France
2. Department of Histology, UFR Leonard de Vinci, University Paris 13, Bobigny, France
3. Department of Pathology, APHP, Avicenne Hospital, Bobigny, France
4. Department of Dermatology, University of Lubeck, Lubeck, Germany
5. Department of Dermatology, University Medical Center Groningen, University of Groningen, Groningen, Netherlands
6. Department of Dermatology, Medical University of Sofia, Sofia, Bulgaria
7. Department of Dermatology and Cutaneous Biology Research Institute, Yonsei University College of Medicine, Gangnam Severance Hospital, Seoul, South Korea
8. Department of Dermatology, Hospital Clinic de Barcelona, Facultat de Medicina, Universitat de Barcelona, Barcelona, Spain
9. Autoimmune Bullous Diseases Research Center, Department of Dermatology, Razi Hospital, Tehran University of Medical Sciences, Tehran, Iran
10. Division of Molecular Dermatology, Department of Dermatology, Paracelsus Medical University Salzburg, Salzburg, Austria
11. Department of Dermatology, University of Iowa and Department of Veterans Affairs Medical Center, Iowa City, IA, United States
12. Department of Dermatology, Duke Medical Center, Durham, NC, United States
13. Department of Dermatology, University Hospital, Marburg, Germany
14. Department of Dermatology, Mayo Clinic, Rochester, MN, United States
15. Department of Dermatology and Venereology, University Hospital Center Zagreb, University of Zagreb School of Medicine, Zagreb, Croatia
16. Second University Dermatology Department, Aristotle University School of Medicine, Papageorgiou General Hospital, Thessaloniki, Greece
17. Department of Dermatology, University of Pennsylvania and Philadelphia Department of Veterans Affairs Medical Center, Philadelphia, PA, United States
18. Department of Dermatology, Keck School of Medicine, University of Southern California, Los Angeles, CA, United States
19. Department of Dermatology at St George Hospital, University of New South Wales, Sydney, Australia

Source: British Journal of Dermatology Published:2018

Abstract

Background: Epidermolysis bullosa acquisita (EBA) is a complex autoimmune bullous disease disease with variable clinical presentations and multiple possible diagnostic tests, making an international consensus on the diagnosis of EBA essential. Objectives: To obtain an international consensus on the clinical and diagnostic criteria for EBA. Methods: The International Bullous Diseases Group (IBDG) met three times to discuss the clinical and diagnostic criteria for EBA. For the final voting exercise, 22 experts from 14 different countries voted on 50 different items. When > 30% disagreed with a proposal, a discussion was held and re-voting carried out. Results: In total, 48 of 50 proposals achieved consensus after discussion. This included nine diagnostic criteria, which are summarized in a flow chart. The IBDG was unable to determine one procedure that would be applicable worldwide. A limitation of the study is that differential diagnosis of bullous systemic lupus erythematosus has not been addressed. Conclusions: This first international consensus conference established generally agreed-upon clinical and laboratory criteria defining the clinical classification of and diagnostic testing for EBA. Holding these voting exercises in person with the possibility of discussion prior to voting has advantages in reaching consensus over Delphi exercises with remote voting. © 2017 British Association of Dermatologists

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Style	Citing Format
MLA	Prostsquarcioni C, et al.. "International Bullous Diseases Group: Consensus on Diagnostic Criteria for Epidermolysis Bullosa Acquisita." British Journal of Dermatology, vol. 179, no. 1, 2018, pp. 30-41.
APA	Prostsquarcioni C, Caux F, Schmidt E, Jonkman MF, Vassileva S, Kim SC, Iranzo P, Daneshpazhooh M, Terra J, Bauer J, Fairley J, Hall R, Hertl M, Lehman JS, Marinovic B, Patsatsi A, Zillikens D, Werth V, Woodley DT, Murrell DF (2018). International Bullous Diseases Group: Consensus on Diagnostic Criteria for Epidermolysis Bullosa Acquisita. British Journal of Dermatology, 179(1), 30-41.
Chicago	Prostsquarcioni C, Caux F, Schmidt E, Jonkman MF, Vassileva S, Kim SC, Iranzo P, et al.. "International Bullous Diseases Group: Consensus on Diagnostic Criteria for Epidermolysis Bullosa Acquisita." British Journal of Dermatology 179, no. 1 (2018): 30-41.
Harvard	Prostsquarcioni C et al. (2018) 'International Bullous Diseases Group: Consensus on Diagnostic Criteria for Epidermolysis Bullosa Acquisita', British Journal of Dermatology, 179(1), pp. 30-41.
Vancouver	Prostsquarcioni C, Caux F, Schmidt E, Jonkman MF, Vassileva S, Kim SC, et al.. International Bullous Diseases Group: Consensus on Diagnostic Criteria for Epidermolysis Bullosa Acquisita. British Journal of Dermatology. 2018;179(1):30-41.
BibTex	@article{ author = {Prostsquarcioni C and Caux F and Schmidt E and Jonkman MF and Vassileva S and Kim SC and Iranzo P and Daneshpazhooh M and Terra J and Bauer J and Fairley J and Hall R and Hertl M and Lehman JS and Marinovic B and Patsatsi A and Zillikens D and Werth V and Woodley DT and Murrell DF}, title = {International Bullous Diseases Group: Consensus on Diagnostic Criteria for Epidermolysis Bullosa Acquisita}, journal = {British Journal of Dermatology}, volume = {179}, number = {1}, pages = {30-41}, year = {2018} }
RIS	TY - JOUR AU - Prostsquarcioni C AU - Caux F AU - Schmidt E AU - Jonkman MF AU - Vassileva S AU - Kim SC AU - Iranzo P AU - Daneshpazhooh M AU - Terra J AU - Bauer J AU - Fairley J AU - Hall R AU - Hertl M AU - Lehman JS AU - Marinovic B AU - Patsatsi A AU - Zillikens D AU - Werth V AU - Woodley DT AU - Murrell DF TI - International Bullous Diseases Group: Consensus on Diagnostic Criteria for Epidermolysis Bullosa Acquisita JO - British Journal of Dermatology VL - 179 IS - 1 SP - 30 EP - 41 PY - 2018 ER -

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