Tehran University of Medical Sciences

Science Communicator Platform

Stay connected! Follow us on X network (Twitter):
Share this content! On (X network) By
Epidermolysis Bullosa With Clinical Manifestations of Sepsis and Pneumonia: A Case Report



Khanmohammadi S1 ; Yousefzadeh R2 ; Rashidan M1 ; Hajibeglo A3 ; Bekmaz K4
Authors
Show Affiliations
Authors Affiliations
  1. 1. Department of Nursing, Ali Abad Katoul Branch, Islamic Azad University, Ali Abad Katoul, Iran
  2. 2. Department of Nursing and Midwifery, Bojnurd University Medical Science, Khorasan Somali, Iran
  3. 3. School of Nursing and Midwifery, Shahid Beheshti University of Medical Sciences, Tehran, Iran
  4. 4. Ziaeian Hospital, Tehran University of Medical Sciences, Tehran, Iran

Source: Journal of Pakistan Association of Dermatologists Published:2021

Abstract

Epidermolysis bullosa is an inherited disease of skin tissues that causes bleeding blisters on the skin and mucosal membrane. This report presents a girl aged 17 months with epidermolysis bullosa with clinical manifestations of sepsis and pneumonia with increased body temperature, anorexia and wheezing. Blood tests include: WBC: 24000 µl, HB: 7.9 mg/dl, ESR: 99, CRP: +2. The patient underwent treatment with ceftriaxone, vancomycin, Hydrocortisone, and paracetamol. Fever of the patient was stopped at the third day of hospitalization, and the ESR reaches 25 and WC reaches 9900 µl. According to the report, it is recommended to consider increase in body temperature and increase in WBC and ESR, and perform required attempts in patients with epidermolysis bullosa. © 2021 Pakistan Association of Dermatologists. All rights reserved.