Epidermolysis Bullosa With Clinical Manifestations of Sepsis and Pneumonia: A Case Report Publisher



Khanmohammadi S¹ ; Yousefzadeh R² ; Rashidan M¹ ; Hajibeglo A³ ; Bekmaz K⁴ Show Affiliations
Source: International Journal of Surgery Case Reports Published:2021

Abstract

Background: Epidermolysis bullosa is an inherited disease that causes bleeding blisters on the skin tissues and mucosal membranes. This study reports a case of epidermolysis bullosa with clinical manifestations of sepsis and pneumonia. Case report: A 17-month-old female with epidermolysis bullosa presented with clinical manifestations of sepsis and pneumonia, including increased body temperature, anorexia, and wheezing. Blood test results included the following: white blood cell (WBC) count, 24,000/μl; hemoglobin level, 7.9 mg/dl; erythrocyte sedimentation rate (ESR), 99 mm/h; and C-reactive protein level, +2. The patient was given ceftriaxone, vancomycin, hydrocortisone, and acetaminophen. The patient's fever resolved on the third day of hospitalization, and the ESR and WBC count reached 25 mm/h and 9900/μl, respectively. Conclusions: According to the report, it is recommended to consider an increase in body temperature, WBC count, and ESR, and perform the required attempts in patients with epidermolysis bullosa. © 2021 The Authors