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Congenital Absence of the Pericardiumin a 16-Year-Oldmale With a Rare Pattern of Involvement



Mostafavi A1 ; Khavandi S1 ; Alizadesani Z2 ; Khavandi S1 ; Tabatabaie SA1
Authors
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Authors Affiliations
  1. 1. Department of Cardiology, Shariati Hospital, Tehran University of Medical Sciences, Tehran, Iran
  2. 2. Department of Cardiology, Rajaie Cardiovascular, Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran

Source: Iranian Heart Journal Published:2015

Abstract

The congenital pericardial defect is a rare malformation that can be complete or partial. This kind of defect is associated with other congenital abnormalities in 30-50% of patients. Whereas the complete absence of the pericardium is mostly asymptomatic and has little clinical importance, partial ones may cause chest pain or dyspnea and can be life-threatening through the strangulation of the cardiac structure. The defect is partial in most cases and is more often left-sided than right-sided. We report a case of the congenital absence of the pericardium around the right ventricle and the posterior portion of the left ventricle without evidence of cardiac chamber herniation or strangulation. © 2015, Iranian Heart Journal. All rights reserved.