Vogt-Koyanagi-Harada Syndrome Presenting With Encephalopathy Publisher



Naeini A¹ ; Daneshmand D¹ ; Khorvash F¹ ; Chitsaz A²
Source: Annals of Indian Academy of Neurology Published:2013

Abstract

VogtKoyanagi-Harada (VKH) is a rare syndrome affecting tissues with melanocytes. The possibility that VKH syndrome has an autoimmune pathogenesis is supported by the high frequency of human leukocyte antigen-DR4 commonly associated with other autoimmune diseases. Eyes are the main affected organ, resulting in blindness. Brain disease as a late onset event is extremely rare. Here, we are reporting a 57-year-old woman with previously diagnosed VKH syndrome, presenting with a late-onset brain encephalopathy. She was treated with corticosteroids and discharged from hospital with good general condition.