Clear Cell Sarcoma: A Case Report and Review of Literature



Abdollahi A¹ ; Khatami F² ; Tavangar SM^{2, 3}
Source: International Journal of Hematology-Oncology and Stem Cell Research Published:2018

Abstract

Clear cell sarcoma (CCS), a deep-rooted tumor with a predilection for lower extremities, has a proclivity to involve the tendons and aponeuroses. This sarcoma is seen predominantly around the foot and ankle region. Diagnosis is mainly finalized using histological and immunohistochemical assessment. The main treatment strategy is surgery followed by chemotherapy. An erratic challenge is posed by histological similarity and immunohistochemical overlap to the diagnosis and distinguishing of clear cell sarcoma from primary or metastatic malignant melanoma (MM) which is more common. Here, we described a CCS case located in the left leg of a 37-year-old male patient. © 2018, Tehran University of Medical Sciences (TUMS). All rights reserved.