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Management of Inborn Errors of Immunity Publisher



Kalmarzi RN1 ; Eslamian MH2 ; Abolhassani H3, 4 ; Aghamohammadi A4 ; Hammarstrom L3 ; Gennery AR5
Authors

Source: Inborn Errors of Immunity: A Practical Guide Published:2021


Abstract

By unifying the diagnostic approach in different medical authority levels, the next step will be the improvement of the clinical therapy and follow-up visit schedules in all patients with different types of primary immunodeficiency disorders. Although for some rare genetic diseases, it is more difficult to find a consensus guideline on the precise modalities because many of them need further patients’ cohort with long-term prognostic analysis. However, regarding frequent clinically diagnosed PIDs, including antibody deficiencies and combined immunodeficiencies, the standard therapeutic protocols should be determined and provided accessibility universally. In this chapter we have provided a general insight about main management and therapeutic modalities for immunodeficient patients. © 2021 Elsevier Inc. All rights reserved.
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